https://scholars.lib.ntu.edu.tw/handle/123456789/476142
標題: | Isolated intestinal transplantation for megacystis microcolon intestinal hypoperistalsis syndrome: Case report | 作者: | Huang C.-M. SHENG-HONG TSENG Weng C.-C. Chen Y. |
關鍵字: | isolated intestinal transplantation; megacystis microcolon intestinal hypoperistalsis syndrome; multivisceral transplantation | 公開日期: | 2013 | 卷: | 17 | 期: | 1 | 起(迄)頁: | E4-E8 | 來源出版物: | Pediatric Transplantation | 摘要: | MMIHS is a rare congenital disease. It is characterized by distended urinary bladder, small colon and intestinal hypoperistalsis, or aperistalsis with normal morphology. There is no specific treatment for MMIHS, and most patients have to be maintained by TPN, which frequently causes TPN-related liver failure, loss of venous access, or catheter-related sepsis. The prognosis of patients with MMIHS is poor, and most patients die early. Multivisceral transplantation including stomach, duodenum, intestine, and liver has been used for the treatment of patients with MMIHS because these patients often have liver failure. We report an eight-yr-old patient with MMIHS who was treated with isolated intestinal transplantation. She had completely oral intake during the four yr of follow-up. The experience in this case suggests isolated intestinal transplantation may be indicated in selected cases with MMIHS. ? 2012 John Wiley & Sons A/S. |
URI: | https://www.scopus.com/inward/record.uri?eid=2-s2.0-84872825005&doi=10.1111%2fpetr.12019&partnerID=40&md5=9f02fe4f3e79cc033073a986fdf890f0 https://scholars.lib.ntu.edu.tw/handle/123456789/476142 |
ISSN: | 1397-3142 | DOI: | 10.1111/petr.12019 | SDG/關鍵字: | serum albumin; tacrolimus; article; autosomal recessive inheritance; case report; child; elemental diet; enteropathy; female; follow up; gastrointestinal transit; human; ileus; immunosuppressive treatment; intestine transplantation; lymphocyte count; parenteral nutrition; perioperative period; prognosis; school child; syndrome MMIH; total parenteral nutrition; Abnormalities, Multiple; Child; Colon; Female; Follow-Up Studies; Humans; Intestinal Pseudo-Obstruction; Intestine, Small; Parenteral Nutrition, Total; Prognosis; Taiwan; Treatment Outcome; Urinary Bladder |
顯示於: | 醫學系 |
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