https://scholars.lib.ntu.edu.tw/handle/123456789/642120
標題: | A case of primary pleural epithelioid hemangioendothelioma achieving stable disease with paclitaxel treatment: A case report and literature review | 作者: | Chou, Chun-Ying Hu, Hsiang-Wei WEI-WU CHEN SHU-YUNG LIN |
關鍵字: | CAMTA1; epithelioid hemangioendothelioma; paclitaxel; pleural effusion; pleural malignancy | 公開日期: | 四月-2024 | 卷: | 12 | 期: | 4 | 來源出版物: | Respirology case reports | 摘要: | Epithelioid hemangioendothelioma (EHE) is a rare vascular neoplasm with a clinical behaviour that falls between a benign hemangioma and a high-grade angiosarcoma. Pleural EHE is exceptionally rare, and its prognosis is grim, with most patients experiencing survival of less than 1 year. Here, we present a case of pleural EHE in a 45-year-old woman with a month-long history of right-sided pleuritic chest pain. Chest computed tomography revealed consolidation, atelectasis of the right lung, right pleural thickening, and pleural effusion. She underwent video-assisted thoracoscopic surgery for decortication and was diagnosed with conclusively pleural EHE, showing a CAMTA1 rearrangement. Paclitaxel treatment, administered once weekly on days 1, 8 and 15 of a 28-day cycle, resulted in a stable disease after 12 cycles. Managing patients with pleural EHE is challenging because there are still no established standard treatments. Our case achieved 11-month progression-free survival following paclitaxel treatment. |
URI: | https://scholars.lib.ntu.edu.tw/handle/123456789/642120 | ISSN: | 2051-3380 | DOI: | 10.1002/rcr2.1341 |
顯示於: | 醫學院附設醫院 (臺大醫院) |
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