Respiratory muscle rest therapy restores pulmonary function in progressive congenital myopathy - A case report
Journal
Tzu Chi Medical Journal
Journal Volume
14
Journal Issue
3
Pages
181-186
Date Issued
2002
Author(s)
Abstract
The respiratory muscle rest program has been widely used in cases of chronic pulmonary dysfunction. However, the results were quite controversial in various studies. Recently we treated a 33-year-old man with nemaline myopathy who presented with recurrent respiratory tract infection and respiratory failure. He was treated initially with continuous mechanical ventilation, but a few weeks later, he only needed noninvasive ventilator support at night. During 3 years of follow up, he was advised to use a nocturnal ventilator to rest his respiratory muscles during sleep. Fewer hospitalizations and normalized blood gas values were noted. In addition, he had improved lung volume and respiratory muscle endurance. It is postulated that respiratory muscle rest therapy might be indicated and of benefit for patients who have weak respiratory muscles due to congenital myopathy.
Subjects
Lung function; Nemaline myopathy; Pulmonary rehabilitation; Respiratory muscle rest
SDGs
Other Subjects
adult; article; artificial ventilation; blood gas analysis; breathing muscle; case report; clinical feature; disease course; endurance; follow up; hospitalization; human; lung function; lung volume; male; muscle fatigue; nemaline myopathy; rest; sleep; treatment outcome; ventilator
Type
journal article