Coexistence of lymphangioleiomyomatosis and angiomyolipomas in a patient of tuberous sclerosis complex: A case report
Journal
Chinese Journal of Radiology
Journal Volume
28
Journal Issue
5
Pages
329-333
Date Issued
2003
Author(s)
Abstract
Pulmonary lymphangioleiomyomatosis (LAM) is a rare disease. The symptoms, radiological features and histopathological evidences are identical to that of pulmonary involvement of tuberous sclerosis complex (TSC). Coexistence of renal angiomyolipomas (AMLs), especially multiple and bilateral sides is often observed. Some investigators have proposed that LAM may be a forme fruste of TSC. We present a case that was firstly diagnosed as LAM and then bilateral multiple renal AMLs were found during pre-transplant evaluation. The case also met the diagnostic criteria of TSC. We discuss the relationship between LAM and TSC.
SDGs
Other Subjects
adult; angiomyolipoma; article; case report; clinical feature; comorbidity; computer assisted tomography; female; human; kidney hemangiomyolipoma; lymphangioleiomyomatosis; pulmonary lymphangioleiomyomatosis; thorax radiography; tuberous sclerosis
Type
journal article