Diffuse neonatal hemangiomatosis complicated with cardiac tamponade: A case report
Journal
Tzu Chi Medical Journal
Journal Volume
11
Journal Issue
1
Pages
103-108
Date Issued
1999
Author(s)
Abstract
Diffuse neonatal hemangiomatosis (DNH) is a rare benign vascular disorder with aggressive clinical behavior in infancy. Clinically, it is characterized by multiple hemangiomas of the skin and visceral organs. The organs most commonly affected are the gastrointestinal tract, liver, lungs, and brain. About 60% of patients die in the first few months of life, due to high-output heart failure, gastrointestinal bleeding and consumption coagulopathy. We report a case of DNH in a male infant. The hemangioma involved skin, gastrointestinal tract, urinary tract, lungs, brain, pleura, meninx and epicardium complicated with persistent gastrointestinal hemorrhage, severe epidural and subdural hemorrhage and Kasabach-Merritt Syndrome. In addition, bleeding from the hemangiomas of the epicardium caused cardiac tamponade. The patient died at 21 months of age despite treatment with corticosteroid and α-interferon. This case indicated that hemangioma of epicardium may cause cardiac tamponade and aggravate the symptoms of heart failure in patient with DNH.
SDGs
Other Subjects
alpha interferon; corticosteroid; article; brain tumor; case report; child death; epicardium; gastrointestinal hemorrhage; gastrointestinal tumor; heart failure; heart tamponade; heart tumor; hemangiomatosis; hemopericardium; human; Kasabach Merritt syndrome; liver tumor; lung tumor; male; meninx disorder; pleura tumor; preschool child; skin hemangioma; spinal cord hemorrhage; urinary tract tumor; vascular disease
Type
journal article