Hypoplastic left heart syndrome with valvular pulmonary stenosis: Successful management with norwood staged reconstruction
Journal
Annals of Thoracic Surgery
Journal Volume
92
Journal Issue
3
Pages
1115-1116
Date Issued
2011
Author(s)
Abstract
The association of hypoplastic left heart syndrome with valvular pulmonary stenosis is rare and is not well-described in the literature. Here we describe the experience of Norwood stage one reconstruction in an infant with hypoplastic left heart syndrome and significant pulmonary stenosis. The baby was successful palliated and stage II reconstruction with a bidirectional Glenn shunt was also later performed. Even though this condition is considered a poor candidate for Norwood stage one reconstruction because of outflow obstruction, Norwood stage one reconstruction was used because neonatal transplantation is not a feasible option in Taiwan. This experience suggested that Norwood staged reconstruction is an option for this difficult condition. ? 2011 The Society of Thoracic Surgeons.
Other Subjects
artery catheterization; article; case report; computer assisted tomography; cyanosis; disease severity; echocardiography; female; Glenn shunt; heart left ventricle outflow tract obstruction; heart septum defect; heart ventricle pressure; human; hypoplastic left heart syndrome; lung blood flow; newborn; Norwood procedure; oxygen saturation; priority journal; pulmonary artery; pulmonary subvalvular stenosis; pulmonary valve insufficiency; tricuspid annuloplasty; Abnormalities, Multiple; Cardiopulmonary Bypass; Diagnosis, Differential; Echocardiography; Female; Follow-Up Studies; Humans; Hypoplastic Left Heart Syndrome; Infant, Newborn; Norwood Procedures; Pregnancy; Pulmonary Valve Stenosis; Ultrasonography, Prenatal
Type
journal article