Electron beam computed tomography appearance of endocardial fibroelastosis EBCT appearance of endocardial fibroelastosis
Journal
International Journal of Cardiovascular Imaging
Journal Volume
19
Journal Issue
1
Pages
85-90
Date Issued
2003
Author(s)
Abstract
Recent reports of endocardial fibroelastosis (EFE) have not reported the disease to be correctly diagnosed during the patients' life spans. Our purpose in this communication is to provide some feasible approaches toward correct diagnosis a the primitive stage and possible correlations to the prognosis. We analyzed five cases of EFE from 1997 to 2001. Four had pathology proven EFE. Data were sampled from the clinical symptoms, electrocardiography, echocardiography, electron beam computed tomography (EBCT), management, and prognosis. A case of anomalous left coronary artery originating from main pulmonary artery diagnosed EFE correctly before death by utilizing an EBCT. The second case was double outlet of the right ventricle with severe calcification and fibrosis shown on EBCT studies, while the third case had severe calcification over both apices. Both patients required heart transplantation. The fourth case, with a decreasing ejection fraction, was idiopathic hypertropic subaortic stenosis with mild calcification and fibrosis on the EBCT images. The last stationary case had severe aortic stenosis with trivial fibrotic change and calcification. We propose that EBCT may accurately help to diagnose EFE before pathology confirmation. The magnitude of calcification and fibrotic thickness in the myocardium of the EBCT imaging may predict the outcome of EFE.
SDGs
Other Subjects
inotropic agent; adult; aorta stenosis; aorta subvalvular stenosis; artery calcification; article; atrioventricular block; autopsy; clinical article; coronary artery anomaly; correlation analysis; data analysis; death; defibrillation; diagnostic accuracy; disease severity; echocardiography; electrocardiography; electron beam tomography; endocardial fibroelastosis; feasibility study; female; follow up; heart ejection fraction; heart hypertrophy; heart murmur; heart muscle; heart muscle fibrosis; heart right ventricle double outlet; heart transplantation; heart ventricle tachycardia; human; infant; left coronary artery; lifespan; male; mitral valve stenosis; outcomes research; pathology; prediction; preschool child; prognosis; pulmonary artery; symptom; tricuspid valve regurgitation; valvuloplasty; Adult; Child; Child, Preschool; Coronary Angiography; Coronary Vessel Anomalies; Diagnosis, Differential; Echocardiography; Endocardial Fibroelastosis; Fatal Outcome; Female; Heart Transplantation; Humans; Infant; Male; Middle Aged; Prognosis; Tomography, X-Ray Computed
Type
journal article