Surgery for fibrosing mediastinitis with severe pulmonary hypertension due to pulmonary venous stenosis
Journal
The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation
Journal Volume
43
Journal Issue
1
Pages
28–31
Date Issued
2024-01
Author(s)
Abstract
A 21-year-old woman with severe pulmonary hypertension and circulatory collapse was referred to our hospital for possible lung transplantation with extracorporeal membrane oxygenation support. Computed tomography revealed severe stenosis of all 4 pulmonary veins, and fibrosing mediastinitis was suspected. Surgical reconstruction of the pulmonary veins was performed, and extracorporeal membrane oxygenation support was weaned off. After surgery, pulmonary vascular resistance normalized. This successful case demonstrates that surgical pulmonary venous reconstruction is an important treatment for fibrosing mediastinitis induced by pulmonary venous stenosis and pulmonary hypertension.
Subjects
Pulmonary venous stenosis
bovine patch repair
extracorporeal membrane oxygenation
fibrosing mediastinitis
pulmonary hypertension
Publisher
Elsevier Inc.
Type
journal article