https://scholars.lib.ntu.edu.tw/handle/123456789/194729
DC 欄位 | 值 | 語言 |
---|---|---|
dc.contributor | 小兒科 | en |
dc.contributor.author | WANG, PEN-JUNG | en |
dc.contributor.author | HWU, WUH-LIANG | en |
dc.contributor.author | YOUNG, CHAINLLIE | en |
dc.contributor.author | YAU, KOU-INN, TSOU | en |
dc.contributor.author | SHEN, YU-ZEN | en |
dc.contributor.author | LEE, WANG-TSO | en |
dc.creator | 王本榮;胡務亮;楊千立;鄒國英;沈友仁;李旺祚 | zh_TW |
dc.creator | WANG, PEN-JUNG;HWU, WUH-LIANG;YOUNG, CHAINLLIE;YAU, KOU-INN, TSOU;SHEN, YU-ZEN;LEE, WANG-TSO | en |
dc.date | 1998 | en |
dc.date.accessioned | 2008-12-10T08:59:17Z | - |
dc.date.accessioned | 2018-07-11T17:52:04Z | - |
dc.date.available | 2008-12-10T08:59:17Z | - |
dc.date.available | 2018-07-11T17:52:04Z | - |
dc.date.issued | 1998 | - |
dc.identifier.uri | http://ntur.lib.ntu.edu.tw//handle/246246/90528 | - |
dc.description.abstract | To re-evaluate the diagnostic criteria for early myoclonic encephalopathy (EME), the following study was done. During the past 2 years, five patients with erratic, fragmentary myoclonus of neonatal onset, in association with other types of seizures, were analyzed with regard to etiologies, electroclinical features and their evolution, using a series of examinations including electroencephalographies (EEGs) and metabolic investigations. Of these five patients, three were diagnosed to have non- ketotic hyperglycinemia (NKH); one was pyridoxine-dependent; the other was cryptogenic. Only two cases (one NKH and one cryptogenic) had initial typical suppression-burst (S-B) EEG pattern, which subsequently evolved into multiple paroxysmal abnormalities with random asynchronous attenuation (MP-AA) pattern. The other two cases with NKH had MP-AA EEG pattern throughout both awake and sleep recordings in two consecutive EEG studies. All three cases with NKH survived with increasing microcephaly, muscle tonicity; all developed infantile spasm with hypsarrhythmia on EEGs . The patient with pyridoxine- dependency had an initial MP-AA EEG pattern , which converted into S-B pattern after the first use of pyridoxine, eventually becoming normal after a supplement with the second-dose of pyridoxine. In conclusion, either S-B or NIP- AA pattern may reflect the severity of the underlying pathologies or the disease stages. These results suggest that, from both etiological and electroclinical viewpoints , EME may represent a broader spectrum than previously recognized. The still ongoing controversy regarding whether the S-B pattern should be recognized as the sore EEG criteria for the diagnosis of EME needs further experience to clarify. (C) 1998 Elsevier Science B.V. All rights reserved . | en |
dc.language | en-us | en |
dc.language.iso | en_US | - |
dc.relation | BRAIN AND DEVELOPMENT v.20 n.7 pp.530-535 | en |
dc.relation.ispartof | BRAIN AND DEVELOPMENT | - |
dc.title | The Controversy Regaring Criteria for Early Myoclonic Encephalopathy | en |
dc.type | journal article | en |
dc.relation.pages | 530-535 | - |
dc.relation.journalvolume | v.20 | - |
dc.relation.journalissue | n.7 | - |
item.openairecristype | http://purl.org/coar/resource_type/c_6501 | - |
item.openairetype | journal article | - |
item.languageiso639-1 | en_US | - |
item.grantfulltext | none | - |
item.cerifentitytype | Publications | - |
item.fulltext | no fulltext | - |
顯示於: | 醫學系 |
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