組織球增多症－X併有廣泛性淋巴結病變－兩病例報告

Abstract

Histiocytosis-X之病例在兒科領域中雖少見，但大家均耳熟能詳。惟其變化多端， 時有特殊病例以不同臨床症狀出現，本文報告兩例是以淋巴結病變爲主要表徽 。其一爲九歲女孩，首先以左腸骨溶骨病灶表現，隨後以淋巴結病變爲 表徽而無其他病灶。其二爲16個月大的女嬰，以腹部腫塊表現，經剖腹手術證 實後腹腔淋巴結腫塊。二例皆經病理切片確定爲 Histiocytosis-X 。 Though Histiocytosis-X is a rare disease in children, it is a well- known disease for pediatricians. Because of its diversity in clinical manifestation, it provides a diagnostic challenge to us. This paper presents two cases of Histiocytosis-X with massive lymph node involvement. One was a 9-year-old girl who suffered from the lytic lesion of left iliac bone initially, followed by cervical lymphadenopathy with. out other symptoms. The other was a 16-month-old female baby with abdominal mass proved to be retroperitoneal lymphadenopathy. The pathological findings of the lymphadenopathy of these two cases were compatible with Histiocytosis -X.