Esophageal Varices in Congenital Heart Disease with Total Anomalous Pulmonary Venous Connection
Resource
INTERNATIONAL JOURNAL OF CARDIAC IMAGING v.16 n.5 pp.405-409
Journal
INTERNATIONAL JOURNAL OF CARDIAC IMAGING
Journal Volume
v.16
Journal Issue
n.5
Pages
405-409
Date Issued
2000
Date
2000
Author(s)
LI, YIU-WAH
WU, MEI-HWAN
CHEN, SHYH- JYE
Abstract
Total anomalous pulmonary venous connection (TAPVC) is an uncommon congenital anomaly in which the anatomical presentations vary widely among patients. We hereby present two newborns with TAPVC associated with asplenia syndrome; both had severe esophageal varices due to infradiaphragmatic pulmonary venous drainage. Ultrafast computed tomography ( CT) scanning was superior to color Doppler echocardiography and cardiac catheterization as it provided a detailed portrait of the pulmonary drainage. The remarkable radiographic manifestations are presented.
Subjects
asplenia syndrome
computed tomography
congenital heart disease
esophageal varices
total anomalous pulmonary venous connection
DIAGNOSIS