Kikuchi Disease Associated with Hemophagocytic Syndrome Presented as Acute Parotitis
Journal
臺灣耳鼻喉頭頸外科雜誌
Journal Volume
47卷
Journal Issue
1期
Pages
68-74
Date Issued
2012
Author(s)
YEE-CHUN CHEN
Abstract
INTRODUCTION: Kikuchi disease (KD), is a rare, benign, self-limiting disease reportedly primarily in Asians. Hemophagocytic syndrome (HPS) is an uncommon hematologic disorder that often results in fatal multi-organ failure. KD has been infrequently reported in association with HPS, particularly presented as acute parotitis.CASE PRESENTATION: A 28-year-old male initially presented with bilateral acute parotitis and persistent fever. Progressive parotid swelling extending into the neck region causing airway obstruction necessitated emergency tracheostomy. Final inguinal lymph node and bone marrow biopsies confirmed the diagnosis of KD accompanied with HPS. Subsequent to supportive therapy, the patient was discharged from the hospital 26 days after admission. One year later, the patient remained asymptomatic without any signs of recurrence.DISCUSSION: KD associated with HPS is rarely reported in otolaryngology. The otolaryngologist should recognize the potential for KD with HPS in atypical lesion of the head and neck. (J Taiwan Otolaryngol Head Neck Surg 2012; 47:68-74)
SDGs
Type
journal article