https://scholars.lib.ntu.edu.tw/handle/123456789/434098
標題: | Clinical spectrum and long-term outcome of ebstein's anomaly based on a 26-year experience in an asian cohort | 作者: | Chang Y.-M. JOU-KOU WANG SHUENN-NAN CHIU MING-TAI LIN EN-TING WU CHUN-AN CHEN SHU-CHIEN HUANG YIH-SHARNG CHEN CHUNG-I CHANG ING-SH CHIU JIUNN-LEE LIN LING-PING LAI MEI-HWAN WU |
公開日期: | 2009 | 卷: | 168 | 期: | 6 | 起(迄)頁: | 685-690 | 來源出版物: | European Journal of Pediatrics | 摘要: | Ebstein's anomaly is a rare, congenital cardiac anomaly that may result in cyanosis, right heart failure, and tachyarrhythmia during the newborn stage or after adolescence. This study investigated the data of 77 patients diagnosed between 1980 and 2006 at a tertiary care center in Taiwan. Patients were grouped into either an early group or a late group. Survival declined rapidly within the newborn stage in the early group, but declined only during the third decade in the late group. Surgical results were poor (20% success rate) for neonatal systemic-to-pulmonary shunts in those cases with associated pulmonary atresia, but were satisfactory for other surgical modes. Supraventricular tachyarrhythmia occurred in 31 (41%) patients at a median age of 10 years and could be eliminated by radiofrequency ablation (81% success rate), though the recurrence rate was high (41%). In conclusion, other than those cases requiring shunts at the newborn stage, the long-term outcome was favorable. ? 2008 Springer-Verlag. |
URI: | https://www.scopus.com/inward/record.uri?eid=2-s2.0-67349101568&doi=10.1007%2fs00431-008-0820-0&partnerID=40&md5=8f08f3f5741082667a0010b14c588d47 https://scholars.lib.ntu.edu.tw/handle/123456789/434098 |
ISSN: | 0340-6199 | DOI: | 10.1007/s00431-008-0820-0 | SDG/關鍵字: | article; disease association; disease course; Ebstein anomaly; heart rhythm; human; priority journal; pulmonary valve atresia; radiofrequency ablation; supraventricular tachycardia; survival rate; systemic pulmonary shunt; Adolescent; Adult; Catheter Ablation; Child; Child, Preschool; Ebstein Anomaly; Female; Humans; Infant; Infant, Newborn; Kaplan-Meiers Estimate; Male; Retrospective Studies; Tachycardia, Supraventricular; Taiwan; Treatment Outcome; Young Adult |
顯示於: | 醫學系 |
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