Gender difference in clinical and genetic characteristics of Brugada syndrome: SADS-TW BrS registry
Journal
QJM : monthly journal of the Association of Physicians
Journal Volume
112
Journal Issue
5
Pages
343–350
Date Issued
2019-05-01
Author(s)
Chen C.-Y.J.
Liao M.-C.
Chen J.-J.
Yeh S.-F.S.
Yang D.-H.
Horie, M
Wu T.-J.
Chen S.-A.
Wang C.-C.
Chang K.-C.
Feng A.-N.
Lin Y.-J.
Ueng K.-C.
Tsao H.-M.
Huang J.-L.
Tsai W.-C.
Tsai C.-F.
Chang S.-L.
Lo L.-W.
Hu Y.-F.
Chung F.-P.
Chang C.-J.
Lo H.-M.
Chiang M.-C.
Hsia C.-P.
Liu J.-F.
Chua S.-K.
Hsieh Y.-C.
Li C.-H.
Liao Y.-C.
Lin H.-H.
Liu Z.-Z.
Ye G.-H.
Chiu W.-R.
Chang J.-R.
Feng W.-J.
Chang S.-X.
Lei M.-H.
Ko W.-C.
Kong C.-W.
Kuo C.-T.
Huang B.-X.
Li K.-T.
Chen W.-D.
Luo J.-L.
Lin J.-Y.
Tsai T.-N.
Hsu C.-T.
Lin L.-R.
Chen R.-Y.
Li P.-T.
Stephen Huang S.K.
SADS-TW BrS Registry
Abstract
Brugada syndrome (BrS) is a heritable sudden cardiac death (SCD) disease with male predominance. Information on gender difference of BrS remains scarce.
Subjects
SUDDEN CARDIAC DEATH; PROLONGED QTC INTERVAL; ST-SEGMENT ELEVATION; BUNDLE-BRANCH BLOCK; POTASSIUM CURRENTS; PREDOMINANCE; PHENOTYPE; MORTALITY; DIAGNOSIS; INWARD
SDGs
Other Subjects
sodium channel Nav1.5; SCN5A protein, human; sodium channel Nav1.5; adult; Article; Brugada syndrome; clinical feature; electrocardiography; faintness; family history; female; gene frequency; gene mutation; genetic trait; Han Chinese; heart rate; heart ventricle fibrillation; heart ventricle tachycardia; human; major clinical study; male; onset age; PR interval; priority journal; QRS complex; QRS interval; QTc interval; Sanger sequencing; sex difference; sudden cardiac death; Taiwan; Brugada syndrome; complication; faintness; genetics; long QT syndrome; middle aged; mutation; pathophysiology; register; risk assessment; sex factor; sex ratio; sudden cardiac death; Adult; Brugada Syndrome; Death, Sudden, Cardiac; Electrocardiography; Female; Humans; Long QT Syndrome; Male; Middle Aged; Mutation; NAV1.5 Voltage-Gated Sodium Channel; Registries; Risk Assessment; Sex Distribution; Sex Factors; Syncope; Taiwan
Publisher
OXFORD UNIV PRESS
Type
journal article