Chiu H.-H.MEI-HWEI CHANGHONG-YUAN HSUYEN-HSUAN NI2021-01-042021-01-0419950277-2116https://www.scopus.com/inward/record.uri?eid=2-s2.0-0029129268&doi=10.1097%2f00005176-199510000-00008&partnerID=40&md5=5068a60a8fa99f75e5cbddb7891e4a18https://scholars.lib.ntu.edu.tw/handle/123456789/537221Three patients with congenital mechanical intestinal obstruction and features of syndromic paucity of the interlobular bile ducts (SPILBD) are presented. Two of them have siblings with syndromic paucity of the interlobular bile ducts. Two patients had jejunoileal atresia, while the other had a meconium plug with intestinal perforation. All subjects underwent surgery for intestinal obstruction within the first 24 h of life. Progressive disappearance of the bile ductules was observed in one case. We believe that an insult such as vascular insufficiency to both bile ductal epithelium and the small intestine may be the cause of this congenital disorder. ? 1995 Lippincott-Raven Publishers, Philadelphia.[SDGs]SDG3adult; article; bile duct malformation; case report; disease association; female; functional anatomy; human; human cell; human tissue; infant; intestine atresia; intestine blood flow; intestine perforation; male; meconium ileus; priority journal; small intestine obstruction; Abnormalities, Multiple; Bile Ducts; Case Report; Female; Human; Infant, Newborn; Intestinal Obstruction; Intestine, Small; Male; Syndromejournal article10.1097/00005176-199510000-0000885232142-s2.0-0029129268