Lai C.-C.HSIAO-HUA CHANGYIN-LIN WANGGUAY-FEN HUANG2021-07-052021-07-0520200917-2394https://www.scopus.com/inward/record.uri?eid=2-s2.0-85092461252&doi=10.1016%2fj.pdj.2020.09.004&partnerID=40&md5=09658e120df11e524201ae52f34de54ahttps://scholars.lib.ntu.edu.tw/handle/123456789/569417Osteogenesis imperfecta (OI) is an autosomal dominant disorder not only influencing the musculoskeletal system but also dentition. This case is a 6 year 2 month old female suffering from severe deforming, type III OI, which is deathful due to frequent bone fractures and hyperthermia. We could observe very short stature, severe scoliosis, hunchback, and bowing of legs from appearance. She visited our clinic due to pain from multiple dental caries and complicated medical status. In the oral cavity, dentinogenesis imperfecta and constriction of maxilla were also presented. With multiple visits, pain was relieved and occlusion was re-established successfully. ? 2020[SDGs]SDG3fluoride varnish; pamidronic acid; Article; body height; body weight; bone density; bone development; case report; child; clinical article; dental caries; dental procedure; female; fever; fracture; general anesthesia; growth curve; human; hyperthermia; kyphosis; limited mobility; low set ear; lumbar spine; malocclusion; maxillary second premolar; mouth examination; open reduction (procedure); osteogenesis imperfecta; osteosynthesis; osteotomy; preschool child; priority journal; scoliosis; short stature; tooth brushing; tooth disease; tooth extraction; tooth pain; tooth radiographyjournal article10.1016/j.pdj.2020.09.0042-s2.0-85092461252