Chuan M.-T.TSEN-FANG TSAIWu M.-C.Wong T.-H.2020-10-222020-10-2219971018-8665https://www.scopus.com/inward/record.uri?eid=2-s2.0-0031031361&doi=10.1159%2f000246061&partnerID=40&md5=ad538f0e12b18610c3b7ce9143267378https://scholars.lib.ntu.edu.tw/handle/123456789/517757Background: Pigmented dermatofibrosarcoma is a rare tumor of the skin and constitutes 1—5% of all dermatofibrosarcoma. Most cases present as polypoid multinodular growth. Occasional cases may be atrophic. We report an extraordinary case with progressive infraorbital atrophy. Observation: A 24-year-old woman came to us for a diffuse bluish atrophic lesion over the left infraorbital area. The lesion progressed gradually over 2 years. Histologic examination revealed mature spindle cell proliferation in the lower dermis and hypodermis. Interspersed were some heavily pigmented melanocytes. Conclusion: We report an unusual case of progressive bluish discoloration and atrophy of the infraorbital area. This is a rare manifestation of dermatofibrosarcoma. ? 1997 S. Karger AG, Basel.[SDGs]SDG3adult; article; atrophic skin disease; case report; cell proliferation; clinical feature; dermatofibrosarcoma protuberans; dermis; differential diagnosis; eye disease; female; human; human tissue; hyperpigmentation; melanocyte; priority journal; spindle cell; subcutaneous tissuejournal article10.1159/00024606190317962-s2.0-0031031361