Huang C.-N.HSIN-HUI YUSHUENN-NAN CHIUJYH-HONG LEELI-CHIEH WANGYAO-HSU YANGBOR-LUEN CHIANG2020-12-082020-12-0820130172-8172https://www.scopus.com/inward/record.uri?eid=2-s2.0-84886605099&doi=10.1007%2fs00296-011-2240-0&partnerID=40&md5=40f8d6867c9e4c8f7113fe84811abbcchttps://scholars.lib.ntu.edu.tw/handle/123456789/525004Acute myocarditis and ventricular arrhythmia are rarely seen as the initial presentation of systemic lupus erythematosus (SLE) in children. We reported the case of a 12-year-old girl with congestive heart failure, acute myocarditis and pericardial effusion as a primary manifestation of SLE. Sudden cardiovascular collapse due to ventricular fibrillation (VF), ventricular tachycardia (VT) and cardiac tamponade occurred. After resuscitation and pericardiocentesis, frequent VF/VT refractory to anti-arrhythmic therapy was supported by venoarterial extracorporeal membrane oxygenation. Early diagnosis and a combination treatment for heart failure, arrhythmias and immunosuppression may result in a favorable outcome. ? Springer-Verlag 2011.[SDGs]SDG3angiotensin receptor antagonist; antiarrhythmic agent; azathioprine; beta adrenergic receptor blocking agent; captopril; digoxin; diuretic agent; furosemide; hydroxychloroquine; methotrexate; methylprednisolone; prednisolone; arteriovenous shunt; article; case report; child; childhood disease; congestive heart failure; early diagnosis; extracorporeal oxygenation; female; heart failure; heart tamponade; heart ventricle fibrillation; heart ventricle tachycardia; human; immunosuppressive treatment; myocarditis; pericardial effusion; pericardiocentesis; priority journal; resuscitation; school child; shock; systemic lupus erythematosus; heart failure; heart ventricle fibrillation; myocarditis; systemic lupus erythematosus; Child; Female; Heart Failure; Humans; Lupus Erythematosus, Systemic; Myocarditis; Ventricular FibrillationAcute myocarditis and ventricular fibrillation as initial presentation of pediatric systemic lupus erythematosusjournal article10.1007/s00296-011-2240-0221199422-s2.0-84886605099