WEI-CHIH LIAOHSIU-PO WANG2021-01-152021-01-152018#VALUE!https://www.scopus.com/inward/record.uri?eid=2-s2.0-85053951950&doi=10.1007%2f978-981-10-8654-0_5&partnerID=40&md5=a2fb5cd5cb2de2a27cac271ecd5784e2https://scholars.lib.ntu.edu.tw/handle/123456789/540924Pancreaticobiliary maljunction (PBM), a congenital anomaly in which the junction of the biliary and pancreatic ducts lies outside of the duodenal wall, has been associated with various biliary diseases, including choledochal cyst, gallblad- der carcinoma, and gallbladder adenomyomatosis. In our study of patients undergo- ing ERCP for pancreaticobiliary conditions in Taiwan, the prevalence of PBM was 8.7%. PBM can be further classified into the B-P type (i.e., the common bile duct joins the pancreatic duct) and P-B type (i.e., the pancreatic duct joins the common bile duct). Choledochal cyst is the most commonly reported biliary disease associ- ated with PBM. In our study, the prevalence of PBM in patients with choledochal cyst and gallbladder cancer were 93.8% and 62.5%, respectively. Notably, PBMs in patients with choledochal cyst were mostly of the B-P type, whereas PBMs in patients with gallbladder carcinoma were mostly of the P-B type. This chapter sum- marizes the literature on PBM from Taiwan. ? Springer Nature Singapore Pte Ltd. 2018.[SDGs]SDG3book part10.1007/978-981-10-8654-0_52-s2.0-85053951950