https://scholars.lib.ntu.edu.tw/handle/123456789/469637
標題: | Scimitar syndrome: Incidence, treatment, and prognosis | 作者: | CHING-CHIA WANG EN-TING WU SHYH-JYE CHEN FRANK LEIGH LU SHU-CHIEN HUANG JOU-KOU WANG CHUNG-I CHANG MEI-HWAN WU |
公開日期: | 2008 | 卷: | 167 | 期: | 2 | 起(迄)頁: | 155-160 | 來源出版物: | European Journal of Pediatrics | 摘要: | This study is based on a database of 16 years; we sought to define the incidence and outcome of scimitar syndrome. Of 8,771 patients, 5 (0.057%) with scimitar syndrome were identified and constituted the study population. Follow-up ranged from 1 to 16 years (median: 10 years). Diagnosis was assured by computed tomography in four patients and by cardiac catheterization in one. Two patients presented with respiratory distress soon after birth and required early pneumonectomy in one case and coil embolization of the abnormal feeding arteries to the right lower lung followed by surgical rerouting of the abnormal pulmonary vein and repair of the atrial septal defect in the other case. The former was supported by ventilator therapy for 3 years after pneumonectomy, but was finally weaned from the ventilator. Among the other three, two had repeated pneumonia that resolved after rerouting of the abnormal right pulmonary vein and cardiac repair. The asymptomatic child did not receive any intervention. In spite of the abnormal orientation of the airways, none of the four patients with detailed computed tomography imaging showed any significant compression of the airways. All five patients were doing well as of the last follow-up. In conclusion, scimitar syndrome is a very rare disease in this Asian country and the varied symptoms, such as tachypnea and repeated infection, could be improved after interventions. ? 2007 Springer-Verlag. |
URI: | https://www.scopus.com/inward/record.uri?eid=2-s2.0-37549017301&doi=10.1007%2fs00431-007-0441-z&partnerID=40&md5=613fecbebede4cdefc5605765a100db4 https://scholars.lib.ntu.edu.tw/handle/123456789/469637 |
ISSN: | 0340-6199 | DOI: | 10.1007/s00431-007-0441-z | SDG/關鍵字: | adolescent; article; artificial ventilation; child; coil embolization; computer assisted tomography; female; follow up; heart atrium septum defect; heart catheterization; heart surgery; human; incidence; infant; lung resection; major clinical study; male; pneumonia; priority journal; prognosis; respiratory distress; scimitar syndrome; tachypnea; Child; Child, Preschool; Embolization, Therapeutic; Female; Follow-Up Studies; Humans; Imaging, Three-Dimensional; Incidence; Infant; Male; Prognosis; Radiography, Thoracic; Scimitar Syndrome; Taiwan; Tomography, X-Ray Computed |
顯示於: | 醫學系 |
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