Infundibular pulmonic stenosis with intact ventricular septum: a report of 15 surgically corrected patients
Journal
International Journal of Cardiology
Journal Volume
41
Journal Issue
2
Pages
115-121
Date Issued
1993
Author(s)
Abstract
Infundibular pulmonic stenosis with intact ventricular septum of primary origin is an uncommon condition. We report 15 such patients (nine males and six females, aged 7-36 years) who had undergone surgical correction for the anomaly during the period between 1975 and 1992. The occurrence of this clinical setting represents 0.19% (15/7826) of all cardiac operations and 0.46% (15/3222) of congenital heart diseases undergoing surgical correction during that period of time. The lesion was of discrete fibromuscular hypertrophy of the infundibulum in all 15 patients. The presenting symptoms of most patients were exertional dyspnea and syncope; however, five patients with severe obstruction were asymptomatic. The peak systolic pressure gradient across the infundibulum ranged from 71 to 230 mmHg. There was only one operative death; the remainder had remained well following the surgery over a mean follow-up period of 35 months. Surgical correction for infundibular pulmonic stenosis is rewarding in the absence of heart failure. ? 1993.
SDGs
Other Subjects
article; case report; child; congenital heart disease; controlled study; echocardiography; electrocardiography; female; fibromuscular dysplasia; heart ventricle septum; human; hypertrophy; male; priority journal; pulmonary valve stenosis; Adolescent; Adult; Arrhythmia; Child; Echocardiography; Electrocardiography; Female; Follow-Up Studies; Heart Septum; Hemodynamics; Human; Male; Pulmonary Subvalvular Stenosis; Ventricular Function, Right
Type
journal article