https://scholars.lib.ntu.edu.tw/handle/123456789/538500
標題: | A variant of long QT syndrome manifested as fetal tachycardia and associated with ventricular septal defect | 作者: | MEI-HWAN WU FON-JOU HSIEH JOU-KOU WANG Kau M.-L. |
公開日期: | 1999 | 出版社: | BMJ Publishing Group | 卷: | 82 | 期: | 3 | 起(迄)頁: | 386-388 | 來源出版物: | Heart | 摘要: | Two patients with a novel variant of long QT syndrome are described. The clinical course was characterised by an in utero onset of ventricular tachycardia and atrio-ventricular block (at 26 and 30 weeks' gestational age, respectively), and an association with a ventricular septal defect. Studies of both patients' families identified relatives with prolonged QT interval, syncope, or sudden death. One patient died of intractable ventricular tachycardia at 4 days old. The other received β blocker treatment and a pacemaker. She died suddenly at the age of 10 months. The unique association with ventricular septal defect and the malignant clinical course warrants further molecular diagnosis of this novel variant of long QT syndrome. |
URI: | https://www.scopus.com/inward/record.uri?eid=2-s2.0-0032845034&doi=10.1136%2fhrt.82.3.386&partnerID=40&md5=b9d95fa5135a77396593ab85d47cf870 https://scholars.lib.ntu.edu.tw/handle/123456789/538500 |
ISSN: | 1355-6037 | DOI: | 10.1136/hrt.82.3.386 | SDG/關鍵字: | lidocaine; propranolol; article; artificial heart pacemaker; atrioventricular block; case report; disease association; echocardiography; female; heart right bundle branch block; heart ventricle septum defect; human; infant; long QT syndrome; newborn; priority journal; sudden death; syncope; torsade des pointes |
顯示於: | 醫學系 |
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