https://scholars.lib.ntu.edu.tw/handle/123456789/539164
標題: | Absent pulmonary valve syndrome in tetralogy of Fallot: report of two cases | 作者: | Yang H.Y. HUNG-CHI LUE JOU-KOU WANG |
公開日期: | 1993 | 卷: | 34 | 期: | 3 | 起(迄)頁: | 228-236 | 來源出版物: | Zhonghua Minguo xiao er ke yi xue hui za zhi [Journal]. Zhonghua Minguo xiao er ke yi xue hui | 摘要: | A combination of absence of the pulmonary valve with ventricular septal defect, annular pulmonary stenosis and aneurysm of the pulmonary artery is called "absent pulmonary valve syndrome". Most patients with this condition suffered from severe respiratory symptoms in early infancy. Respiratory failure which is the leading cause of mortality in infants with this syndrome, results from pulmonary emphysema, pulmonary atelectasis or pulmonary infection as a consequence of compression of the bronchus by the pulmonary aneurysm. If these patients can be treated medically to survive beyond one year old, gradual decrease in severity of symptoms is expected. A definite correction in childhood is recommended. Otherwise, palliative operation in infancy has a high mortality rate. This paper reported two cases with severe symptoms in infancy; one patient expired at nine months of age, and the other lived beyond one year to receive surgical correction at the age of three. The etiology, clinical features and treatment of absent pulmonary valve syndrome are also discussed. |
URI: | https://www.scopus.com/inward/record.uri?eid=2-s2.0-0027604649&partnerID=40&md5=ab6f9e8ce63ff4c6133ec3d7480ff75b https://scholars.lib.ntu.edu.tw/handle/123456789/539164 |
ISSN: | 0001-6578 | SDG/關鍵字: | aneurysm; article; case report; congenital malformation; Fallot tetralogy; female; heart septum defect; human; infant; male; multiple malformation syndrome; newborn; pulmonary artery; pulmonary valve; pulmonary valve stenosis; syndrome; Abnormalities, Multiple; Aneurysm; Female; Heart Septal Defects, Ventricular; Humans; Infant; Infant, Newborn; Male; Pulmonary Artery; Pulmonary Valve; Pulmonary Valve Stenosis; Syndrome; Tetralogy of Fallot |
顯示於: | 醫學系 |
在 IR 系統中的文件,除了特別指名其著作權條款之外,均受到著作權保護,並且保留所有的權利。