Bedtime extended release cornstarch improves biochemical profile and sleep quality for patients with glycogen storage disease type Ia

Patients with glycogen storage disease type Ia (GSDIa) are prone to hypoglycemia. Uncooked cornstarch (CS) is the treatment, but maintaining nighttime blood glucose levels is still difficult.

Subjects

Pittsburgh sleep quality index (PSQI); continuous glucose monitoring (CGM); extended release cornstarch (ER-CS); glycogen storage disease type Ia (GSDIa)